Ectopia cordis is an extremely rare lethal anomaly characterized with heart located partially or completely outside the thoracic cavity. 0t can be isolated anomaly or as a component of complex syndromes including supraumbilical abdominal wall defect, deficiency of the anterior diaphragm and congenital intracardiac defects as shown in the figure. Further details can be seen in the article by Başar et al. in this issue.