Volume 30, Issue 5 pp. 528-530

A case of Schöpf–Schulz–Passarge syndrome

P. J. Hampton,

P. J. Hampton

Departments of Dermatology and Pathology, Royal Victoria Infirmary, Queen Victoria Road, Newcastle upon Tyne, UK

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B. Angus,

B. Angus

Departments of Dermatology and Pathology, Royal Victoria Infirmary, Queen Victoria Road, Newcastle upon Tyne, UK

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A. J. Carmichael,

A. J. Carmichael

Department of Dermatology, The James Cook University Hospital, Middlesbrough, UK

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P. J. Hampton,

P. J. Hampton

Departments of Dermatology and Pathology, Royal Victoria Infirmary, Queen Victoria Road, Newcastle upon Tyne, UK

Search for more papers by this author

B. Angus,

B. Angus

Departments of Dermatology and Pathology, Royal Victoria Infirmary, Queen Victoria Road, Newcastle upon Tyne, UK

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A. J. Carmichael,

A. J. Carmichael

Department of Dermatology, The James Cook University Hospital, Middlesbrough, UK

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First published: 05 July 2005

https://doi.org/10.1111/j.1365-2230.2005.01855.x

Citations: 40

Dr P. J. Hampton, Department of Dermatology, Royal Victoria Infirmary, Queen Victoria Road, Newcastle upon Tyne, UK.
E-mail: [email protected]

Conflict of interest: none declared.

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Summary

Schöpf–Schulz–Passarge syndrome (SSPS) is a rare ectodermal dysplasia characterized by hypodontia, hypotrichosis, nail dystrophy, palmoplantar keratoderma, and periocular and eyelid margin apocrine hidrocystomas. Several other skin tumours have been described in association with this syndrome, in particular, multiple palmoplantar eccrine syringofibroadenoma (ESFA). We report a case of SSPS with diffuse palmoplantar hyperkeratosis, which was shown by histology and immunocytochemistry to be due to ESFA.

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Volume30, Issue5

September 2005

Pages 528-530

A case of Schöpf–Schulz–Passarge syndrome

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Citing Literature

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A case of Schöpf–Schulz–Passarge syndrome

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