Biliary drainage as treatment for allograft steatosis following liver transplantation for PFIC-1 disease: A single-center experience
Leina S. Alrabadi
Department of Pediatrics, Section of Pediatric Gastroenterology and Hepatology, Yale University School of Medicine, New Haven, CT, USA
Search for more papers by this authorRaffaella A. Morotti
Department of Pathology, Yale University School of Medicine, New Haven, CT, USA
Search for more papers by this authorPamela L. Valentino
Department of Pediatrics, Section of Pediatric Gastroenterology and Hepatology, Yale University School of Medicine, New Haven, CT, USA
Search for more papers by this authorManuel I. Rodriguez-Davalos
Department of Surgery, Section of Transplantation and Immunology, Yale University School of Medicine, New Haven, CT, USA
Search for more papers by this authorUdeme D. Ekong
Department of Pediatrics, Section of Pediatric Gastroenterology and Hepatology, Yale University School of Medicine, New Haven, CT, USA
Search for more papers by this authorCorresponding Author
Sukru H. Emre
Department of Surgery, Section of Transplantation and Immunology, Yale University School of Medicine, New Haven, CT, USA
Correspondence
Sukru Emre, Department of Surgery, Section of Transplantation and Immunology, Yale University School of Medicine, New Haven, CT, USA.
Email: [email protected]
Search for more papers by this authorLeina S. Alrabadi
Department of Pediatrics, Section of Pediatric Gastroenterology and Hepatology, Yale University School of Medicine, New Haven, CT, USA
Search for more papers by this authorRaffaella A. Morotti
Department of Pathology, Yale University School of Medicine, New Haven, CT, USA
Search for more papers by this authorPamela L. Valentino
Department of Pediatrics, Section of Pediatric Gastroenterology and Hepatology, Yale University School of Medicine, New Haven, CT, USA
Search for more papers by this authorManuel I. Rodriguez-Davalos
Department of Surgery, Section of Transplantation and Immunology, Yale University School of Medicine, New Haven, CT, USA
Search for more papers by this authorUdeme D. Ekong
Department of Pediatrics, Section of Pediatric Gastroenterology and Hepatology, Yale University School of Medicine, New Haven, CT, USA
Search for more papers by this authorCorresponding Author
Sukru H. Emre
Department of Surgery, Section of Transplantation and Immunology, Yale University School of Medicine, New Haven, CT, USA
Correspondence
Sukru Emre, Department of Surgery, Section of Transplantation and Immunology, Yale University School of Medicine, New Haven, CT, USA.
Email: [email protected]
Search for more papers by this authorAbstract
Development of macrovesicular steatosis post–LT in patients with PFIC-1 is increasingly being observed, with the etiology not fully understood. We highlight successful and effective EBD for reversal of allograft steatosis in 2 patients with PFIC-1 disease and discuss our experience with internal biliary diversion in this patient population.
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