Editorial
Protecting the allograft following liver transplantation for PFIC1
First published: 26 August 2016
No abstract is available for this article.
References
- 1Srivastava A. Progressive familial intrahepatic cholestasis. J Clin Exp Hepatol. 2014; 4: 25–36.
- 2Cai SY, Gautam S, Nguyen T, Soroka CJ, Rahner C, Boyer JL. ATP8B1 deficiency disrupts the bile canalicular membrane bilayer structure in hepatocytes, but FXR expression and activity are maintained. Gastroenterology. 2009; 136: 1060–1069.
- 3Verhulst PM, van der Velden LM, Oorschot V, et al. A flippase-independent function of ATP8B1, the protein affected in familial intrahepatic cholestasis type 1, is required for apical protein expression and microvillus formation in polarized epithelial cells. Hepatology. 2010; 51: 2049–2060.
- 4Bull LN, van Eijk MJ, Pawlikowska L, et al. A gene encoding a P-type ATPase mutated in two forms of hereditary cholestasis. Nat Genet. 1998; 18: 219–224.
- 5Klomp LW, Vargas JC, van Mil SW, et al. Characterization of mutations in ATP8B1 associated with hereditary cholestasis. Hepatology. 2004; 40: 27–38.
- 6Linton KJ. Lipid flopping in the liver. Biochem Soc Trans. 2015; 43: 1003–1010.
- 7van der Mark VA, de Waart DR, Ho-Mok KS, et al. The lipid flippase heterodimer ATP8B1-CDC50A is essential for surface expression of the apical sodium-dependent bile acid transporter (SLC10A2/ASBT) in intestinal Caco-2 cells. Biochim Biophys Acta. 2014; 1842: 2378–2386.
- 8Alissa FT, Jaffe R, Shneider BL. Update on progressive familial intrahepatic cholestasis. J Pediatr Gastroenterol Nutr. 2008; 46: 241–252.
- 9Miyagawa-Hayashino A, Egawa H, Yorifuji T, et al. Allograft steatohepatitis in progressive familial intrahepatic cholestasis type 1 after living donor liver transplantation. Liver Transpl. 2009; 15: 610–618.
- 10Nicastro E, Stephenne X, Smets F, et al. Recovery of graft steatosis and protein-losing enteropathy after biliary diversion in a PFIC 1 liver transplanted child. Pediatr Transplant. 2012; 16: E177–E182.
- 11Mali VPFA, Shigeta T, Uchida H, et al. Total internal biliary diversion during liver transplantation for type 1 progressive familial intrahepatic cholestasis: a novel approach. Pediatr Transplant. 2016; 20: 981–986.
- 12Morris AL, Bukauskas K, Sada RE, Shneider BL. Byler disease: early natural history. J Pediatr Gastroenterol Nutr. 2015; 60: 460–466.
- 13van der Woerd WL, Kokke FT, van der Zee DC, Houwen RH. Total biliary diversion as a treatment option for patients with progressive familial intrahepatic cholestasis and Alagille syndrome. J Pediatr Surg. 2015; 50: 1846–1849.