Review Article
Absence of Left Pulmonary Artery in Tetralogy of Fallot with Absent Pulmonary Valve Syndrome
Mustafa Kemal Avsar M.D.,
Tolga Demir M.D.,
Hale Bolgi Demir M.D.,
Mustafa Kemal Avsar M.D.
Department of Cardiovascular Surgery, Medicana International Hospital, Istanbul, Turkey
Search for more papers by this authorCorresponding Author
Tolga Demir M.D.
Department of Cardiovascular Surgery, Beylikduzu Kolan Hospital, Istanbul, Turkey
Address for correspondence: Tolga Demir, M.D., Adnan Kahveci Mah, Osmanli Cad, No. 23, Gurpinar, 34528 Beylikduzu, Istanbul, Turkey. Fax: +90-212-855-75-70; e-mail: [email protected]Search for more papers by this authorHale Bolgi Demir M.D.
Department of Cardiovascular Surgery, Medicana International Hospital, Istanbul, Turkey
Search for more papers by this authorMustafa Kemal Avsar M.D.,
Tolga Demir M.D.,
Hale Bolgi Demir M.D.,
Mustafa Kemal Avsar M.D.
Department of Cardiovascular Surgery, Medicana International Hospital, Istanbul, Turkey
Search for more papers by this authorCorresponding Author
Tolga Demir M.D.
Department of Cardiovascular Surgery, Beylikduzu Kolan Hospital, Istanbul, Turkey
Address for correspondence: Tolga Demir, M.D., Adnan Kahveci Mah, Osmanli Cad, No. 23, Gurpinar, 34528 Beylikduzu, Istanbul, Turkey. Fax: +90-212-855-75-70; e-mail: [email protected]Search for more papers by this authorHale Bolgi Demir M.D.
Department of Cardiovascular Surgery, Medicana International Hospital, Istanbul, Turkey
Search for more papers by this authorConflict of interest: The authors acknowledge no conflict of interest in the submission.
Abstract
The rare combination of tetralogy of Fallot (TOF), absent pulmonary valve syndrome (APVS), and absent left pulmonary artery (ALPA) is reviewed herein. Children with TOF with APVS and ALPA should be closely monitored, even if they are asymptomatic or mildly symptomatic, and should undergo elective surgery at the end of infancy. doi: 10.1111/jocs.12461 (J Card Surg 2015;30:104–107)
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