Airway management of patient with Smith–Lemli–Opitz syndrome for gastric surgery: case report

A case of term, 5-day-old boy, with low birth weight of 2.4 kg, with Smith–Lemli–Opitz syndrome (SLOS) who was first scheduled for gastrostomy tube placement and later for pylorotomy, is discussed. General appearance of face and small chin showed possible difficulties during intubation, which are well known from the literature. Anesthetic plan included possibility of fiberoptic intubation. Mask induction and ventilation had been successful but attempts to intubate patient using fiberoptic bronchoscope had not been feasible and both procedures had been performed using laryngeal mask airway (LMA#1) with spontaneous ventilation without complications. In this case, we are showing the ability to secure the airway in a small infant with SLOS using LMA and the possibility to perform successfully surgery on the gastrointestinal tract.