Brief Report

Pinch-off syndrome in patients with sickle cell disease receiving erythrocytapheresis

Corresponding Author

Rachelle Nuss MD

[email protected]

Department of Pediatric Hematology, The Children's Hospital and the University of Colorado at Denver Health Sciences Center, Denver, Colorado

Colorado Sickle Cell Treatment and Research Center, University of Colorado at Denver Health Sciences Center, Denver, Colorado

1056 E. 19th Ave. Box B-115, Denver, CO 80218.===Search for more papers by this author

Laura Cole RN,

Laura Cole RN

Colorado Sickle Cell Treatment and Research Center, University of Colorado at Denver Health Sciences Center, Denver, Colorado

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Tuan Le MD,

Tuan Le MD

Department of Pathology, The Children's Hospital, Denver, Colorado

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Edmund Orsini MD,

Edmund Orsini MD

Department of Pathology, The Children's Hospital, Denver, Colorado

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Roger Harned MD,

Roger Harned MD

Department of Radiology, The Children's Hospital and the University of Colorado at Denver Health Sciences Center, Denver, Colorado

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Rachelle Nuss MD,

Corresponding Author

Rachelle Nuss MD

[email protected]

Department of Pediatric Hematology, The Children's Hospital and the University of Colorado at Denver Health Sciences Center, Denver, Colorado

Colorado Sickle Cell Treatment and Research Center, University of Colorado at Denver Health Sciences Center, Denver, Colorado

1056 E. 19th Ave. Box B-115, Denver, CO 80218.===Search for more papers by this author

Laura Cole RN,

Laura Cole RN

Colorado Sickle Cell Treatment and Research Center, University of Colorado at Denver Health Sciences Center, Denver, Colorado

Search for more papers by this author

Tuan Le MD,

Tuan Le MD

Department of Pathology, The Children's Hospital, Denver, Colorado

Search for more papers by this author

Edmund Orsini MD,

Edmund Orsini MD

Department of Pathology, The Children's Hospital, Denver, Colorado

Search for more papers by this author

Roger Harned MD,

Roger Harned MD

Department of Radiology, The Children's Hospital and the University of Colorado at Denver Health Sciences Center, Denver, Colorado

Search for more papers by this author

First published: 07 November 2006

https://doi.org/10.1002/pbc.21058

Citations: 3

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Abstract

A 6-year-old female with homozygous sickle cell disease had a central venous access device (CVAD) placed to facilitate chronic erythrocytapheresis. Erythrocytapheresis was ineffective due to the rare pinch-off syndrome causing communication between the dual lumen tubing. Awareness of and monitoring for the pinch-off syndrome is indicated in people with sickle cell disease and a CVAD for chronic erythrocytapheresis. Pediatr Blood Cancer 2008;50:354–356. © 2006 Wiley-Liss, Inc.

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Volume50, Issue2

February 2008

Pages 354-356

Pinch-off syndrome in patients with sickle cell disease receiving erythrocytapheresis

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Pinch-off syndrome in patients with sickle cell disease receiving erythrocytapheresis

Abstract

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