Normal vitamin E status in spinal muscular atrophy

Corresponding Author

Dr Ronald J. Sokol MD

Division of Pediatric Gastroenterology and Nutrition, Children's Hospital Research Foundation, Elland and Bethesda Aves, Cincinnati, OH 45229

Division of Pediatric Gastroenterology and Nutrition, Children's Hospital Research Foundation, Elland and Bethesda Aves, Cincinnati, OH 45229Search for more papers by this author

Susan T. Iannaccone MD,

Susan T. Iannaccone MD

Division of Neurology, Children's Hospital Research Foundation, Elland and Bethesda Aves, Cincinnati, OH 45229

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Dr Ronald J. Sokol MD,

Corresponding Author

Dr Ronald J. Sokol MD

Division of Pediatric Gastroenterology and Nutrition, Children's Hospital Research Foundation, Elland and Bethesda Aves, Cincinnati, OH 45229

Division of Pediatric Gastroenterology and Nutrition, Children's Hospital Research Foundation, Elland and Bethesda Aves, Cincinnati, OH 45229Search for more papers by this author

Susan T. Iannaccone MD,

Susan T. Iannaccone MD

Division of Neurology, Children's Hospital Research Foundation, Elland and Bethesda Aves, Cincinnati, OH 45229

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First published: March 1983

https://doi.org/10.1002/ana.410130318

Citations: 2

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Abstract

In an attempt to confirm prior reports of vitamin E deficiency in Werdnig-Hoffmann disease, we assessed vitamin E nutritional status in 11 children and 6 adults with spinal muscular atrophy (SMA). Serum vitamin E levels (10.6 ± 3.3 m̈g/ml for those less than 12 years old, 13.2 ± 4.5 for those older than 12) and the ratio of serum vitamin E to total serum lipids were normal in all patients. Vitamin E nutritional status appears to be normal in SMA, and vitamin E therapy is not indicated.

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Volume13, Issue3

March 1983

Pages 328-331

Normal vitamin E status in spinal muscular atrophy

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Normal vitamin E status in spinal muscular atrophy

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