Clear cell ependymoma: a mimicker of oligodendroglioma – report of three cases
Deepali Jain
Department of Pathology, All India Institute of Medical Sciences (AIIMS), New Delhi, India
Search for more papers by this authorMehar Chand Sharma
Department of Pathology, All India Institute of Medical Sciences (AIIMS), New Delhi, India
Search for more papers by this authorReena Arora
Department of Pathology, All India Institute of Medical Sciences (AIIMS), New Delhi, India
Search for more papers by this authorChitra Sarkar
Department of Pathology, All India Institute of Medical Sciences (AIIMS), New Delhi, India
Search for more papers by this authorVaishali Suri
Department of Pathology, All India Institute of Medical Sciences (AIIMS), New Delhi, India
Search for more papers by this authorDeepali Jain
Department of Pathology, All India Institute of Medical Sciences (AIIMS), New Delhi, India
Search for more papers by this authorMehar Chand Sharma
Department of Pathology, All India Institute of Medical Sciences (AIIMS), New Delhi, India
Search for more papers by this authorReena Arora
Department of Pathology, All India Institute of Medical Sciences (AIIMS), New Delhi, India
Search for more papers by this authorChitra Sarkar
Department of Pathology, All India Institute of Medical Sciences (AIIMS), New Delhi, India
Search for more papers by this authorVaishali Suri
Department of Pathology, All India Institute of Medical Sciences (AIIMS), New Delhi, India
Search for more papers by this authorAbstract
Clear cell variant of ependymoma is a rare entity which morphologically mimics oligodendroglioma and poses a diagnostic dilemma. We describe three cases of clear cell ependymoma in male children which were supratentorial in location. On microscopic examination, these tumors were composed of sheets of clear cells and resembled oligodendroglioma. Electron microscopy confirmed the ependymal nature of these tumors. Clear cell ependymomas are rare and aggressive tumors. More cases need to be reported to determine their therapeutic responsiveness and prognosis.
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