An unusual case of extra-abdominal desmoid tumour
Abstract
ZAMPIERI N., CECCHETTO M., ZORZI M.G., PIETROBELLI A., OTTOLENGHI A. & CAMOGLIO F. (2010) European Journal of Cancer Care19, 410–412An unusual case of extra-abdominal desmoid tumour
Desmoid tumour is relatively rare and generally non-metastatisizing lesion of mesenchymal origin composed of fibrous tissue and fitting in the group of aggressive fibromatosis; it is a locally aggressive proliferative soft-tissue lesion with controversial nature. This tumour accounts for 0.03% of all tumours and 3% of soft-tissue tumours with annual incidence of two to four cases per million. Although desmoid tumours are more common in persons aged 10–40 years than in others, they do occur in young children and older adults; in children the sex incidence is equal. This is a rare case of extra-abdominal desmoid tumour in a 14-year-old girl affected by spastic tetraparesis. To our knowledge no similar cases are present in literature to date.
