Successful venoarterial extracorporeal membrane oxygenation for prolonged hepatopulmonary syndrome following pediatric liver transplantation: A case report and review of the literature
Hamza Hassan Khan
Transplant Institute, Medstar Georgetown University Hospital, Washington, DC, USA
Search for more papers by this authorLaura Schroeder
Critical Care Medicine, Childrens National Medical Center, Washington, DC, USA
Search for more papers by this authorMegha S. Fitzpatrick
Transplant Institute, Medstar Georgetown University Hospital, Washington, DC, USA
Search for more papers by this authorStuart S. Kaufman
Transplant Institute, Medstar Georgetown University Hospital, Washington, DC, USA
Search for more papers by this authorNada A. Yazigi
Transplant Institute, Medstar Georgetown University Hospital, Washington, DC, USA
Search for more papers by this authorGregory K. Yurasek
Critical Care Medicine, Childrens National Medical Center, Washington, DC, USA
Search for more papers by this authorDavid M. Steinhorn
Critical Care Medicine, Childrens National Medical Center, Washington, DC, USA
Search for more papers by this authorThomas M. Fishbein
Transplant Institute, Medstar Georgetown University Hospital, Washington, DC, USA
Search for more papers by this authorCorresponding Author
Khalid M. Khan
Transplant Institute, Medstar Georgetown University Hospital, Washington, DC, USA
Correspondence
Khalid M. Khan, Transplant Institute, Medstar Georgetown University Hospital, Washington, DC, USA.
Email: [email protected]
Search for more papers by this authorHamza Hassan Khan
Transplant Institute, Medstar Georgetown University Hospital, Washington, DC, USA
Search for more papers by this authorLaura Schroeder
Critical Care Medicine, Childrens National Medical Center, Washington, DC, USA
Search for more papers by this authorMegha S. Fitzpatrick
Transplant Institute, Medstar Georgetown University Hospital, Washington, DC, USA
Search for more papers by this authorStuart S. Kaufman
Transplant Institute, Medstar Georgetown University Hospital, Washington, DC, USA
Search for more papers by this authorNada A. Yazigi
Transplant Institute, Medstar Georgetown University Hospital, Washington, DC, USA
Search for more papers by this authorGregory K. Yurasek
Critical Care Medicine, Childrens National Medical Center, Washington, DC, USA
Search for more papers by this authorDavid M. Steinhorn
Critical Care Medicine, Childrens National Medical Center, Washington, DC, USA
Search for more papers by this authorThomas M. Fishbein
Transplant Institute, Medstar Georgetown University Hospital, Washington, DC, USA
Search for more papers by this authorCorresponding Author
Khalid M. Khan
Transplant Institute, Medstar Georgetown University Hospital, Washington, DC, USA
Correspondence
Khalid M. Khan, Transplant Institute, Medstar Georgetown University Hospital, Washington, DC, USA.
Email: [email protected]
Search for more papers by this authorAbstract
HPS is a major complicating feature of end-stage liver disease. Diagnosis is clinical, and LT is the only definitive treatment. While the general impression is that HPS improves quickly after transplantation, it may not always be the case. We describe the smallest reported child with HPS prior to LT and requiring prolonged venoarterial extracorporeal membrane oxygenation after LT; especially as it is a rare occurrence, physician managing such cases should be aware of the circumstances under which HPS may require specific treatment.
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