Volume 35, Issue 4 pp. e87-e90

CASE REPORT

Fetal and Neonatal Presentation of Long QT Syndrome

RUKMINI KOMARLU M.D.,

RUKMINI KOMARLU M.D.

Department of Pediatric Cardiology, Children's Hospital of Pittsburgh of UPMC, Pittsburgh, Pennsylvania

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LEE BEERMAN M.D.,

LEE BEERMAN M.D.

Department of Pediatric Cardiology, Children's Hospital of Pittsburgh of UPMC, Pittsburgh, Pennsylvania

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DAVID FREEMAN M.D.,

DAVID FREEMAN M.D.

Department of Pediatric Cardiology, St. Vincent Medical Center, Pittsburgh, Pennsylvania

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GAURAV ARORA M.D.,

Corresponding Author

GAURAV ARORA M.D.

Department of Pediatric Cardiology, Children's Hospital of Pittsburgh of UPMC, Pittsburgh, Pennsylvania

Address for reprints: Gaurav Arora, M.D., Children's Hospital of Pittsburgh of UPMC, One Children's Hospital Drive, 4401 Penn Avenue, Pittsburgh, PA 15224. Fax: 412-692-5410; e-mail: [email protected]Search for more papers by this author

RUKMINI KOMARLU M.D.,

RUKMINI KOMARLU M.D.

Department of Pediatric Cardiology, Children's Hospital of Pittsburgh of UPMC, Pittsburgh, Pennsylvania

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LEE BEERMAN M.D.,

LEE BEERMAN M.D.

Department of Pediatric Cardiology, Children's Hospital of Pittsburgh of UPMC, Pittsburgh, Pennsylvania

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DAVID FREEMAN M.D.,

DAVID FREEMAN M.D.

Department of Pediatric Cardiology, St. Vincent Medical Center, Pittsburgh, Pennsylvania

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GAURAV ARORA M.D.,

Corresponding Author

GAURAV ARORA M.D.

Department of Pediatric Cardiology, Children's Hospital of Pittsburgh of UPMC, Pittsburgh, Pennsylvania

First published: 14 March 2011

https://doi.org/10.1111/j.1540-8159.2011.03040.x

Citations: 12

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Abstract

This report describes a fetus presenting with intrauterine tachycardia and hydrops fetalis. Soon after birth the neonate was noted to be in torsades de pointes that responded dramatically to medical management. Long QT syndrome (LQTS) was diagnosed on electrocardiogram obtained soon after birth. The prognosis is poor when LQTS presents in utero or during the first week of life. However, our infant did well with medical management and has remained free of arrhythmias at follow-up. PACE 2012; 35:e87–e90)

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Volume35, Issue4

April 2012

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