Invited Reviews
Evaluation and Management of Persistent Problems After Surgery for Hirschsprung Disease in a Child
Roshni Dasgupta,
Jacob C Langer,
Roshni Dasgupta
Division of Pediatric and Thoracic Surgery, Cincinnati Childrens Hospital Medical Center, Cincinnati, Ohio
Search for more papers by this authorCorresponding Author
Jacob C Langer
Division of Pediatric General Surgery, Hospital for Sick Children, Toronto, Canada
Address correspondence and reprint requests to Jacob C. Langer, MD, Division of Pediatric General Surgery, Room 1526, Hospital for Sick Children, 555 University Ave, Toronto, ON M5G1X8, Canada (e-mail [email protected]).Search for more papers by this authorRoshni Dasgupta,
Jacob C Langer,
Roshni Dasgupta
Division of Pediatric and Thoracic Surgery, Cincinnati Childrens Hospital Medical Center, Cincinnati, Ohio
Search for more papers by this authorCorresponding Author
Jacob C Langer
Division of Pediatric General Surgery, Hospital for Sick Children, Toronto, Canada
Address correspondence and reprint requests to Jacob C. Langer, MD, Division of Pediatric General Surgery, Room 1526, Hospital for Sick Children, 555 University Ave, Toronto, ON M5G1X8, Canada (e-mail [email protected]).Search for more papers by this authorThe authors report no conflicts of interest.
ABSTRACT
Hirschsprung disease occurs approximately once in every 5000 live-born infants. It is characterized by the absence of ganglion cells in the myenteric and submucosal plexuses of the intestine. Once the diagnosis of Hirschprung disease has been made, most patients are now treated with a transanal approach to resection. We review the early and late postoperative complications. Late complications include persistent mechanical obstruction, recurrent or acquired aganglionosis, disordered motility in the proximal colon or small bowel, internal sphincter achalasia, or functional megacolon caused by stool-holding behavior. These children require complex interdisciplinary care to ensure an adequate quality of life.
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