Formation of 2,3-pristenic acid and 3-hydroxypristanic acid from pristanic acid in human liver
N. M. Verhoeven
Department of Clinical Chemistry, Free University Hospital Amsterdam, Amsterdam, The Netherlands
Search for more papers by this authorD. S. M. Schor
Department of Clinical Chemistry, Free University Hospital Amsterdam, Amsterdam, The Netherlands
Search for more papers by this authorG. A. Jansen
Departments of Clinical Chemistry and Pediatrics, University of Amsterdam, Academic Medical Center, Amsterdam, The Netherlands
Search for more papers by this authorR. M. Kok
Department of Clinical Chemistry, Free University Hospital Amsterdam, Amsterdam, The Netherlands
Search for more papers by this authorH. J. ten Brink
Department of Clinical Chemistry, Free University Hospital Amsterdam, Amsterdam, The Netherlands
Search for more papers by this authorR. J. A. Wanders
Departments of Clinical Chemistry and Pediatrics, University of Amsterdam, Academic Medical Center, Amsterdam, The Netherlands
Search for more papers by this authorC. Jakobs
Department of Clinical Chemistry, Free University Hospital Amsterdam, Amsterdam, The Netherlands
Search for more papers by this authorN. M. Verhoeven
Department of Clinical Chemistry, Free University Hospital Amsterdam, Amsterdam, The Netherlands
Search for more papers by this authorD. S. M. Schor
Department of Clinical Chemistry, Free University Hospital Amsterdam, Amsterdam, The Netherlands
Search for more papers by this authorG. A. Jansen
Departments of Clinical Chemistry and Pediatrics, University of Amsterdam, Academic Medical Center, Amsterdam, The Netherlands
Search for more papers by this authorR. M. Kok
Department of Clinical Chemistry, Free University Hospital Amsterdam, Amsterdam, The Netherlands
Search for more papers by this authorH. J. ten Brink
Department of Clinical Chemistry, Free University Hospital Amsterdam, Amsterdam, The Netherlands
Search for more papers by this authorR. J. A. Wanders
Departments of Clinical Chemistry and Pediatrics, University of Amsterdam, Academic Medical Center, Amsterdam, The Netherlands
Search for more papers by this authorC. Jakobs
Department of Clinical Chemistry, Free University Hospital Amsterdam, Amsterdam, The Netherlands
Search for more papers by this author
REFERENCES
- 1Rasmussen JT, Börchers T, Knutsen J (1990) Comparison of the binding affinities of acyl-CoA-binding protein and fatty acid binding protein for long-chain acyl-CoA esters. Biochem J, 265: 849–855.
- 2Ten Brink HJ, Stellaard F, van denHeuvel CMM et al (1992) Pristanic acid and phytanic acid in plasma from patients with peroxisomal disorders: stable isotope dilution analysis with electron capture negative ion mass fragmentography. J Lipid Res, 33: 41–47.
- 3Wanders RJA, Ten Brink HJ, vanRoermund CWT, Schutgens RBH, Tager JM, Jakobs C (1990) Identification of pristanoyl-CoA oxidase activity in human liver and its deficiency in the Zellweger syndrome. Biochem Biophys Res Commun, 172: 490–495.
10.1016/0006-291X(90)90699-N Google Scholar
- 4Wanders RJA, Van Roermund CWT, Schor DSM, tenBrink HJ, Jakobs C (1994) 2-Hydroxyphytanic acid oxidase activity in rat and human liver and its deficiency in the Zellweger syndrome. Biochim Biophys Acta, 1227: 177–182.
- 5Wanders RJA, Denis S, Ruiter JPN, Schutgens RBH, Van Roermund CWT, Jakobs BS (1995) Measurement of peroxisomal fatty acid β-oxidation in cultured human skin fibroblasts. J Inher Metab Dis, 18 (supplement1): 113–124.
10.1007/BF00711434 Google Scholar
