Short Communication
Study of Pathogenesis in Twitcher Mouse, an Enzymatically Authentic Model of Human Krabbe's Disease
K. Inui,
K. Inui
Department of Pediatrics, Osaka University, Fukushima-ku, Osaka, 553 Japan
Search for more papers by this author J. Nishimoto,
J. Nishimoto
Department of Pediatrics, Osaka University, Fukushima-ku, Osaka, 553 Japan
Search for more papers by this author M. Taniike,
M. Taniike
Department of Pediatrics, Osaka University, Fukushima-ku, Osaka, 553 Japan
Search for more papers by this author M. Midorikawa,
M. Midorikawa
Department of Pediatrics, Osaka University, Fukushima-ku, Osaka, 553 Japan
Search for more papers by this author H. Tsukamoto,
H. Tsukamoto
Department of Pediatrics, Osaka University, Fukushima-ku, Osaka, 553 Japan
Search for more papers by this author S. Okada,
S. Okada
Department of Pediatrics, Osaka University, Fukushima-ku, Osaka, 553 Japan
Search for more papers by this author H. Yabuuchi,
H. Yabuuchi
Department of Pediatrics, Osaka University, Fukushima-ku, Osaka, 553 Japan
Search for more papers by this author
K. Inui,
K. Inui
Department of Pediatrics, Osaka University, Fukushima-ku, Osaka, 553 Japan
Search for more papers by this author J. Nishimoto,
J. Nishimoto
Department of Pediatrics, Osaka University, Fukushima-ku, Osaka, 553 Japan
Search for more papers by this author M. Taniike,
M. Taniike
Department of Pediatrics, Osaka University, Fukushima-ku, Osaka, 553 Japan
Search for more papers by this author M. Midorikawa,
M. Midorikawa
Department of Pediatrics, Osaka University, Fukushima-ku, Osaka, 553 Japan
Search for more papers by this author H. Tsukamoto,
H. Tsukamoto
Department of Pediatrics, Osaka University, Fukushima-ku, Osaka, 553 Japan
Search for more papers by this author S. Okada,
S. Okada
Department of Pediatrics, Osaka University, Fukushima-ku, Osaka, 553 Japan
Search for more papers by this author H. Yabuuchi,
H. Yabuuchi
Department of Pediatrics, Osaka University, Fukushima-ku, Osaka, 553 Japan
Search for more papers by this author
First published: April 1989
No abstract is available for this article.
References
- 1Igisu H, Suzuki K (1984) Progressive accumulation of toxic metabolite in a genetic leukodystrophy. Science, 224: 753–755, .
- 2Kobayashi Y, Nagara H, Suzuki K, Suzuki K (1982) The twitcher mouse: Determination of genetic status by galactosylceramidase assay on clipped tail. Biochem. Med., 27: 8–14, .
- 3Neskovic N M, Roussel G, Nussbaum J L (1986) UDP-galactose: Ceramide galactosyltransferase of rat brain: A new method of purification and production of specific antibodies. J. Neurochem., 47: 1412–1418, .
- 4Suzuki K, Suzuki Y, Stanbury J B, Frederickson D S, Goldstein J L, Brown M S (1983) Galactosylceramide lipidosis: Globoid cell leukodystrophy (Krabbe's disease). In: The Metabolic Basis of Inherited Disease, New York: McGraw-Hill, 857–880.
- 5Svennerholm L, Vanier M-T, Manson J-E (1980) Krabbe disease: a galactosylsphingosine (psychosine) lipidosis. J. Lipid Res., 21: 53–64.
