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Opitz (BBB/G) syndrome: Oral manifestations
John K. Brooks D.D.S.,
Claire O. Leonard,
Peter J. Coccaro Jr.,
Corresponding Author
John K. Brooks D.D.S.
Department of Oral Medicine and Diagnostic Sciences, Baltimore College of Dental Surgery, Dental School, University of Maryland, Baltimore, Maryland
Department of Oral Medicine and Diagnostic Sciences, Baltimore College of Dental Surgery, Dental School, University of Maryland at Baltimore, 666 West Baltimore Street, Baltimore, MD 21201Search for more papers by this authorClaire O. Leonard
Department of Pediatrics, University of Utah, School of Medicine, Salt Lake City, Utah
Search for more papers by this authorJohn K. Brooks D.D.S.,
Claire O. Leonard,
Peter J. Coccaro Jr.,
Corresponding Author
John K. Brooks D.D.S.
Department of Oral Medicine and Diagnostic Sciences, Baltimore College of Dental Surgery, Dental School, University of Maryland, Baltimore, Maryland
Department of Oral Medicine and Diagnostic Sciences, Baltimore College of Dental Surgery, Dental School, University of Maryland at Baltimore, 666 West Baltimore Street, Baltimore, MD 21201Search for more papers by this authorClaire O. Leonard
Department of Pediatrics, University of Utah, School of Medicine, Salt Lake City, Utah
Search for more papers by this authorAbstract
We studied a new case of the G (Opitz BBB/G) syndrome in a 12-year-old boy. Several relatives had partial manifestations of the disorder. A comprehensive dental evaluation of the propositus was conducted; included is, to our knowledge, the first published cephalometric analysis of a G syndrome patient. We reviewed 139 cases of the G syndrome; 48 of them had at least one oral abnormality. These included clefting, micrognathia, ankyloglossia, and high-arched palate. Male G syndrome patients are more likely to have oral anomalies than affected females. © 1992 Wiley-Liss, Inc.
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