Chapter 49
Pulmonary Artery Sling
Christian Apitz MD,
Christoph Döhlemann MD,
Jürgen Apitz MD,
Christian Apitz MD
Pediatric Cardiology, Pediatric Heart Centre, University Children's Hospital, Giessen, Germany
Search for more papers by this authorChristoph Döhlemann MD
Division of Pediatric Cardiology, Dr. von Haunersches Kinderspital, University of Munich, Munich, Germany
Search for more papers by this authorJürgen Apitz MD
Division of Pediatric Cardiology, University Children's Hospital, Tübingen, Germany
Search for more papers by this authorChristian Apitz MD,
Christoph Döhlemann MD,
Jürgen Apitz MD,
Christian Apitz MD
Pediatric Cardiology, Pediatric Heart Centre, University Children's Hospital, Giessen, Germany
Search for more papers by this authorChristoph Döhlemann MD
Division of Pediatric Cardiology, Dr. von Haunersches Kinderspital, University of Munich, Munich, Germany
Search for more papers by this authorJürgen Apitz MD
Division of Pediatric Cardiology, University Children's Hospital, Tübingen, Germany
Search for more papers by this authorBook Editor(s):James H. Moller MD,
Julien I. E. Hoffman MD, FRCP,
James H. Moller MD
University of Minnesota, Minneapolis, MN, USA
Search for more papers by this authorJulien I. E. Hoffman MD, FRCP
University of California San Francisco, San Francisco, CA, USA
Search for more papers by this authorFirst published: 13 January 2012
Summary
Infants with a pulmonary artery sling often present with severe respiratory symptoms and distress. These result from compression of the trachea in the area of the carina and right main stem bronchus by the left pulmonary artery which arises from the right pulmonary artery and passes over the right main stem bronchus and behind the trachea to enter the left lung. Diagnosis can be made by identifying on a lateral view esophogram a round mass between the trachea and mid-part of the esophagus. Because tracheal anomalies are associated and need an operation, other imaging or bronchoscopy is necessary to identify them. Treatment is to reattach the left pulmonary artery to the main pulmonary artery and resect associated tracheal stenosis if needed.
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