Chapter 74
Cystic Tumors Other than IPMN
When to Observe, When to Operate, and Optimal Surgical Approach
John W. Kunstman,
James J. Farrell,
John W. Kunstman
Department of Surgery, Section of Surgical Oncology, Yale University School of Medicine, New Haven, CT, USA
VA Connecticut Health System, Department of Veterans Affairs, West Haven, CT, USA
Search for more papers by this authorJames J. Farrell
Yale Pancreatic Disease Program, Interventional Endoscopy and Pancreatic Disease, Yale University School of Medicine, New Haven, CT, USA
Search for more papers by this authorJohn W. Kunstman,
James J. Farrell,
John W. Kunstman
Department of Surgery, Section of Surgical Oncology, Yale University School of Medicine, New Haven, CT, USA
VA Connecticut Health System, Department of Veterans Affairs, West Haven, CT, USA
Search for more papers by this authorJames J. Farrell
Yale Pancreatic Disease Program, Interventional Endoscopy and Pancreatic Disease, Yale University School of Medicine, New Haven, CT, USA
Search for more papers by this authorBook Editor(s):J. Enrique Domínguez-Muñoz MD, PhD,
J. Enrique Domínguez-Muñoz MD, PhD
Director
Department of Gastroenterology and Hepatology, University Hospital of Santiago de Compostela, Santiago de Compostela, Spain
Search for more papers by this authorFirst published: 16 April 2021
Summary
Management of cystic lesions of the pancreas can represent one of the most vexing clinical issues faced by the pancreatic specialist. The natural history of these lesions can range from wholly benign to overt malignancy, further increasing the anxiety of both practitioner and patient. This chapter addresses these dilemmas and presents a framework for successful management of these neoplastic cystic lesions. The most common premalignant cystic lesion of the pancreas is intraductal papillary mucinous neoplasm (IPMN). The chapter focuses on cystic neoplasms of the pancreas other than IPMN, such as mucinous cystic neoplasm (MCN), serous cystadenoma, cystic pancreatic endocrine neoplasms, solid pseudopapillary neoplasm, and other less common lesions. Longitudinal series demonstrate that only a minority of cystic lesions ultimately undergo surgical intervention. MCNs are one of two frequently encountered mucin-containing lesions of the pancreas, the other being IPMN.
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